Article
Lymphocytic vasculitis in X-linked lymphoproliferative disease.
Blood - 1 Jan 2001
Dutz J P, Benoit L, Wang X, Demetrick D J, Junker A, de Sa D, Tan R
Abstract excerpt
Systemic vasculitis is an uncommon manifestation of X-linked lymphoproliferative disease (XLP), a disorder in which there is a selective immune deficiency to Epstein-Barr virus (EBV). The molecular basis for XLP has recently been ascribed to mutations within SLAM-associated protein (SAP), an SH2 domain-containing protein expressed primarily in T cells. The authors describe a patient who died as a result of...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.