Article

Cognitive test performance in CLN3 Disease is associated with the CLN3 Staging System (CLN3SS)

2026-05-24

Abstract excerpt

<h4>Summary</h4> CLN3 disease is an inherited neurodegenerative disease, typically with childhood onset, and characterized by vision loss, seizures, cognitive decline, and difficulties. The CLN3 Staging System (CLN3SS) characterizes disease progression. Our aim was to assess differences in cognitive test scores in relation to CLN3SS among individuals with CLN3 disease. We evaluated the relationship between cognit...

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Literature Corpus work: f755c863-d849-50a6-81c1-74eff43df3ca
DOI: 10.64898/2026.05.21.26353662

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