Article

VEXAS syndrome, immunodeficiency, and risk of infection

2025-10-10

Abstract excerpt

<title>Abstract</title> <p><bold>Background: </bold>VEXAS syndrome is a recently described X-linked somatic autoinflammatory syndrome which manifests with exaggerated hyperinflammation, an MDS-like syndrome, and probable immunodeficiency. <bold>Objective:</bold> The objective of this study is to describe the clinical presentation and outcomes of patients with VEXAS syndrome with a focus on immunodeficiency and in...

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Literature Corpus work: ec20cfba-13a3-595c-a153-645581eac094
DOI: 10.21203/rs.3.rs-7593592/v1

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