Article
Serious infections in patients with VEXAS syndrome: data from the French VEXAS registry.
Annals of the rheumatic diseases - 15 Feb 2024
de Valence Benjamin, Delaune Marion, Nguyen Yann, Jachiet Vincent, Heiblig Mael, Jean Alexis, Riescher Tuczkiewicz Stanislas, Henneton Pierrick, Guilpain Philippe, Schleinitz Nicolas, Le Guenno Guillaume, Lobbes Hervé, Lacombe Valentin, Ardois Samuel, Lazaro Estibaliz, Langlois Vincent, Outh Roderau, Vinit Julien, Martellosio Jean-Philippe, Decker Paul, Moulinet Thomas, Dieudonné Yannick, Bigot Adrien, Terriou Louis, Vlakos Alexandre, de Maleprade Baptiste, Denis Guillaume, Broner Jonathan, Kostine Marie, Humbert Sebastien, Lifermann Francois, Samson Maxime, Pechuzal Susann, Aouba Achille, Kosmider Olivier, Dion Jeremie, Grosleron Sylvie, Bourguiba Rim, Terrier Benjamin, Georgin-Lavialle Sophie, Fain Olivier, Mekinian Arsène, Morgand Marjolaine, Comont Thibault, Hadjadj Jerome
Abstract excerpt
INTRODUCTION: Vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome is an acquired autoinflammatory monogenic disease with a poor prognosis whose determinants are not well understood. We aimed to describe serious infectious complications and their potential risk factors. METHODS: Retrospective multicentre study including patients with VEXAS syndrome from the French VEXAS Registry. Episodes of...
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