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Clinical Presentation of Left Ventricular Noncompaction Cardiomyopathy and Bradycardia in Three Families Carrying <em>HCN4</em> Pathogenic Variants

2022-02-21

Abstract excerpt

<h4>Background: </h4> Left ventricular noncompaction (LVNC) is a genetically and phenotypically heterogeneous cardiomyopathy characterized by a two-layered myocardium consisting of compacted and noncompacted segments, prominent ventricular trabeculations, and intertrabecular recesses. Patients with LVNC are at increased risk to develop heart failure, atrial and ventricular arrhythmias, and/or systemic thromboembol...

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Literature Corpus work
e177e5a8-4227-5c2a-80e1-83aa71804e03
DOI
10.20944/preprints202202.0243.v1
Open publication

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