Article

Clinical Outcome of Children with Progressive Familial Intrahepatic Cholestasis: A Cohort Study

2024-11-27

Abstract excerpt

<title>Abstract</title> <p><bold>Background</bold>: Progressive Familial Intrahepatic Cholestasis (PFIC) is a rare genetic liver disorder characterized by cholestasis and progressive liver damage, often leading to cirrhosis and liver transplantation. Understanding the clinical course and outcomes of PFIC is crucial for improving management strategies, particularly in resource-limited settings like Iran. This stud...

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Literature Corpus work: 8d24c932-a38f-5b55-8536-502cef8eb362
DOI: 10.21203/rs.3.rs-5347230/v1

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