Article

A rare metastatic mesenteric malignant PEComa with TSC2 mutation treated with palliative surgical resection and nab-sirolimus: A case report

2022-10-31

Abstract excerpt

<h4>Background: </h4> Malignant perivascular epithelioid cell tumors (PEComas) are exceedingly rare mesenchymal malignant neoplasms with characteristic morphological and immunohistochemical (IHC) patterns. However, some malignant PEComas are particularly poorly differentiated and may demonstrate atypical histopathological findings, making a definitive diagnosis difficult. PEComas are most commonly found in females...

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Literature Corpus work: 890f3189-1617-5854-b0c0-bd818f422e6b
DOI: 10.21203/rs.3.rs-2204130/v1

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