Article

Characterization of Variably Protease-Sensitive Prionopathy by Capillary Electrophoresis

2024-09-18

Abstract excerpt

<title>Abstract</title> <p>Variably Protease Sensitive Prionopathy (VPSPr) is a rare human prion disease that, like Creutzfeldt-Jakob disease (CJD), results in the deposition of abnormally folded prion protein aggregates in the brain and ultimate fatality. Neuropathology and clinical features of VPSPr are heterogeneous. However, the key discriminating feature is the relative sensitivity of the pathological prion...

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Literature Corpus work: 7a2a2ca9-96c3-57db-b550-a33bb4f6d6c7
DOI: 10.21203/rs.3.rs-4461902/v1

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