Article

Successful Cochlear Implantation in a Patient With Wolfram Syndrome Type 1: a case report

2026-05-11

Abstract excerpt

<title>Abstract</title> <p> <bold>Background</bold> Wolfram syndrome type 1 (DIDMOAD) is a rare autosomal recessive neurodegenerative disorder characterized by early-onset diabetes mellitus, optic atrophy, and progressive sensorineural hearing loss. Management of profound deafness in these patients is challenging, and outcomes of cochlear implantation remain variable. <bold>Case presentation</bold> We report...

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Literature Corpus work: 6429f010-f859-5936-86ce-362e11215a9e
DOI: 10.21203/rs.3.rs-9646524/v1

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