Article

Surgery with emicizumab prophylaxis for two pediatric patients with severe haemophilia A with inhibitors

2020-11-12

Abstract excerpt

Emicizumab is a prophylaxis for patients with severe haemophilia A with inhibitor. Despite the daily prophylaxis, coagulation states stay below normal value and cannot be assessed by standard hemostasis techniques. In our two patients, we use thrombin generation assay (endogenous thrombin potential (ETP) and Peak) to monitor the patient’s clotting status. Under emicizumab, it is needed to add by-passing agent such...

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Literature Corpus work: 48a13e22-22a5-5eea-87ce-2e0fe4139ab9
DOI: 10.22541/au.160516627.75032448/v1

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