Article

Pulmonary features and stage of disease in adult patients with hyper-IgE syndrome: A single-centre clinical study and literature review

2025-04-17

Abstract excerpt

<title>Abstract</title> <p>Background The hyper-IgE syndromes (HIES) are a heterogeneous group of inborn errors of immunity-sharing manifestations including increased infection susceptibility, eczema, and raised serum IgE. Pulmonary complications are responsible for high morbidity and mortality rates in patients with HIES. This study examines the progression of pulmonary disease in adult patients with HIES and c...

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Literature Corpus work: 375765dc-5f23-5a78-abf5-94975d108b43
DOI: 10.21203/rs.3.rs-5618843/v1

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