Article

Lymphoma arising in the setting of inborn errors of immunity: A six-case series of XMEN-associated pediatric lymphoma

2026-08-14

Abstract excerpt

<title>Abstract</title> <p> <bold>Background</bold> Inborn errors of immunity (IEIs), formerly termed primary immunodeficiencies (PIDs), frequently predispose affected individuals to early-onset, recurrent malignant neoplasms as a core clinical hallmark. X-linked immunodeficiency with magnesium defect, Epstein-Barr virus (EBV) infection, and neoplasia (XMEN) represents an ultra-rare X-linked recessive IEI drive...

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Literature Corpus work: 23e097c7-ff43-512c-8767-4edd6209a08d
DOI: 10.21203/rs.3.rs-10382310/v1

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