Article

Altered hematopoietic system and self-tolerance in Bardet-Biedl Syndrome

2020-02-25

Abstract excerpt

Bardet-Biedl Syndrome (BBS) is a pleiotropic genetic disease caused by dysfunction of primary cilia. The immune system of patients with BBS or another ciliopathy has not been investigated, most likely because hematopoietic cells do not form cilia. However, there are multiple indications that the impairment of the processes typically associated with cilia might influence the hematopoietic compartment and immunity....

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Literature Corpus work: 1f594936-04c9-5b59-b700-ba3e5b4cdcee
DOI: 10.1101/2020.02.24.962886

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