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Article

Generalized atrophic benign epidermolysis bullosa.

Advances in dermatology - 1 Jan 1997

Darling T N, Bauer J W, Hintner H, Yancey K B

Abstract excerpt

Junctional EB was once considered a uniformly fetal autosomal recessive skin disease. One of the first and best characterized forms of generalized JEB that has a more favorable prognosis was GABEB. Since its initial description in 1976, many additional cases have been compiled, all sharing the features of chronic blistering from birth, nail dystrophy, hair loss, and abnormal teeth. In addition, some patients have...

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PMID: 9551142

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

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