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Article

Hearing loss in the RBF/DnJ mouse, a proposed animal model of Usher syndrome type IIa.

Hearing research - 1 Oct 1997

Pieke-Dahl S, Ohlemiller K K, McGee J, Walsh E J, Kimberling W J

Abstract excerpt

The Usher syndromes (US) are a group of inherited disorders that feature autosomal recessive neurosensory hearing loss or deafness with retinitis pigmentosa (RP). Moderate to severe non-progressive high frequency hearing loss with RP and normal vestibular function describes Usher syndrome type IIa, which has been localized to 1q41. Severe retinal degeneration in the inbred mouse strain RBF/DnJ is caused by rd3, a...

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PMID: 9367224
DOI: 10.1016/s0378-5955(97)00087-7

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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