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Article

alpha 1-antitrypsin deficiency and idiopathic pulmonary fibrosis in a family.

Southern medical journal - 1 Oct 1996

Kim H, Lepler L, Daniels A, Phillips Y

Abstract excerpt

Idiopathic pulmonary fibrosis (IPF) is an interstitial lung disease of unknown etiology with an estimated prevalence of 3 to 5 per 100,000. We describe a patient with a family history of both IPF and alpha 1-antitrypsin (AAT) deficiency. The patient had a 6-month history of worsening dyspnea when...

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Identifiers

PMID: 8865799
DOI: 10.1097/00007611-199610000-00017

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 4 Sept 2026. Prepared record publication-8865799-2026-09-04.2. Manifest publication-graph-cohort-2026-09-04.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 4 Sept 2026.

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