Article
Familial idiopathic pulmonary fibrosis.
Advances in experimental medicine and biology - 1 Jan 2013
Wytrychowski K, Hans-Wytrychowska A, Nowakowska B
Abstract excerpt
Idiopathic pulmonary fibrosis (IPF) is a progressive interstitial lung disease of unknown etiology, with an appearance of usual interstitial pneumonia on lung biopsy. To-date, about a 100 families diagnosed with IPF have been described. Familial IPF is defined as histologically confirmed IPF occurring in two or more members of a family. Familial pulmonary fibrosis is hereditary, most probably as a feature which...
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