Article
Congenital pulmonary lymphangiectasis with chylothorax: a heterogeneous lymphatic vessel abnormality.
American journal of medical genetics - 1 Aug 1993
Moerman P, Vandenberghe K, Devlieger H, Van Hole C, Fryns J P, Lauweryns J M
Abstract excerpt
We report on 7 perinatal autopsy cases of primary congenital pulmonary lymphangiectasis (CPL) with bilateral chylothorax. This study demonstrates that primary CPL is often complicated by chylous pleural effusions with ensuing pulmonary hypoplasia. Conversely, CPL appears to be a constant pathological finding in spontaneous congenital chylothorax. These observations indicate a common pathogenesis for both...
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