Article
Langerhans'-cell histiocytosis (histiocytosis X)--a clonal proliferative disease.
The New England journal of medicine - 21 Jul 1994
Willman C L, Busque L, Griffith B B, Favara B E, McClain K L, Duncan M H, Gilliland D G
Abstract excerpt
BACKGROUND: The lesions of Langerhans'-cell histiocytosis (histiocytosis X), a proliferative histiocytic disorder of unknown cause, contain histiocytes similar in phenotype to dendritic Langerhans' cells. The disease ranges in severity from a fatal leukemia-like disorder to an isolated lytic lesion of bone. Intermediate forms of the disease are usually characterized by multiorgan involvement, diabetes insipidus,...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.