Article
Phenotypes and outcome of diffuse pulmonary non-amyloid light chain deposition disease.
Respiratory research - 10 Apr 2024
Lestelle François, Beigelman Catherine, Rotzinger David, Si-Mohamed Salim, Nasser Mouhamad, Wemeau Lidwine, Hirschi Sandrine, Prevot Grégoire, Roux Antoine, Bunel Vincent, Gomez Emmanuel, Sohier Laurent, Pradier Helene Morisse, Gaubert Martine Reynaud, Gondouin Anne, Lazor Romain, Glerant Jean-Charles, Bejui Françoise Thivolet, Colombat Magali, Cottin Vincent
Abstract excerpt
BACKGROUND: Light chain deposition disease (LCDD) is a very rare entity. Clinical manifestations of LCDD vary according to the organs involved. Data on pulmonary LCDD are scarce and limited to small series or case reports. This study aimed to describe the characteristics and outcome of diffuse pulmonary non-amyloid LCDD localized to the lungs. STUDY DESIGN AND METHODS: A multicenter retrospective cohort study was...
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