Article
AA amyloidosis complicating cryopyrin-associated periodic syndrome: a study of 86 cases including 23 French patients and systematic review.
Rheumatology (Oxford, England) - 28 Nov 2022
Rodrigues François, Cuisset Laurence, Cador-Rousseau Bérangère, Giurgea Irina, Neven Benedicte, Buob David, Quartier Pierre, Hachulla Eric, Lequerré Thierry, Cam Gérard, Boursier Guilaine, Hervieu Valérie, Grateau Gilles, Georgin-Lavialle Sophie
Abstract excerpt
OBJECTIVE: Cryopyrin-associated periodic syndrome (CAPS) is a rare but treatable inherited autoinflammatory condition including familial cold autoinflammatory syndrome (FCAS), Muckle-Wells syndrome (MWS) and chronic infantile neurologic cutaneous articular syndrome (CINCA). Our objective was to describe the main features of CAPS AA amyloidosis (AA-CAPS) associated and the efficacy of IL-1 inhibitors in this...
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