Article
Recognition, Evaluation, and Management of Pediatric Hereditary Angioedema.
Pediatric emergency care - 1 Apr 2021
Krack Andrew T, Bernstein Jonathan A, Ruddy Richard M
Abstract excerpt
ABSTRACT: Hereditary angioedema (HAE) is a rare, often underrecognized genetic disorder caused by either a C1 esterase inhibitor deficiency (type 1) or mutation (type 2). This leads to overproduction of bradykinin resulting in vasodilation, vascular leakage, and transient nonpitting angioedema occurring most frequently in the face, neck, upper airway, abdomen, and/or extremities. Involvement of the tongue and...
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