Article
Overview of hereditary angioedema caused by C1-inhibitor deficiency: assessment and clinical management.
European annals of allergy and clinical immunology - 1 Feb 2013
Bork K, Davis-Lorton M
Abstract excerpt
Hereditary angioedema due to C1-inhibitor deficiency (HAE-C1-INH) is a rare, autosomal-dominant disease. HAE-C1-INH is characterized by recurrent attacks of marked, diffuse, nonpitting and nonpruritic skin swellings, painful abdominal attacks, and laryngeal edema. The extremities and the gastrointestinal tract are most commonly affected. Swelling of the upper respiratory mucosa poses the greatest risk because...
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