Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond.

doi:10.1016/j.jaci.2004.06.047

Article

Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond.

The Journal of allergy and clinical immunology - 1 Sept 2004

Agostoni Angelo, Aygören-Pürsün Emel, Binkley Karen E, Blanch Alvaro, Bork Konrad, Bouillet Laurence, Bucher Christoph, Castaldo Anthony J, Cicardi Marco, Davis Alvin E, De Carolis Caterina, Drouet Christian, Duponchel Christiane, Farkas Henriette, Fáy Kálmán, Fekete Béla, Fischer Bettina, Fontana Luigi, Füst George, Giacomelli Roberto, Gröner Albrecht, Hack C Erik, Harmat George, Jakenfelds John, Juers Mathias, Kalmár Lajos, Kaposi Pál N, Karádi István, Kitzinger Arianna, Kollár Tímea, Kreuz Wolfhart, Lakatos Peter, Longhurst Hilary J, Lopez-Trascasa Margarita, Martinez-Saguer Inmaculada, Monnier Nicole, Nagy István, Németh Eva, Nielsen Erik Waage, Nuijens Jan H, O'grady Caroline, Pappalardo Emanuela, Penna Vincenzo, Perricone Carlo, Perricone Roberto, Rauch Ursula, Roche Olga, Rusicke Eva, Späth Peter J, Szendei George, Takács Edit, Tordai Attila, Truedsson Lennart, Varga Lilian, Visy Beáta, Williams Kayla, Zanichelli Andrea, Zingale Lorenza

Abstract excerpt

Hereditary angioedema (HAE), a rare but life-threatening condition, manifests as acute attacks of facial, laryngeal, genital, or peripheral swelling or abdominal pain secondary to intra-abdominal edema. Resulting from mutations affecting C1 esterase inhibitor (C1-INH), inhibitor of the first complement system component, attacks are not histamine-mediated and do not respond to antihistamines or corticosteroids....

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