Article
Preventive medicine of von Hippel-Lindau disease-associated pancreatic neuroendocrine tumors.
Endocrine-related cancer - 1 Sept 2018
Krauss Tobias, Ferrara Alfonso Massimiliano, Links Thera P, Wellner Ulrich, Bancos Irina, Kvachenyuk Andrey, Villar Gómez de Las Heras Karina, Yukina Marina Y, Petrov Roman, Bullivant Garrett, von Duecker Laura, Jadhav Swati, Ploeckinger Ursula, Welin Staffan, Schalin-Jäntti Camilla, Gimm Oliver, Pfeifer Marija, Ngeow Joanne, Hasse-Lazar Kornelia, Sansó Gabriela, Qi Xiaoping, Ugurlu M Umit, Diaz Rene E, Wohllk Nelson, Peczkowska Mariola, Aberle Jens, Lourenço Delmar M, Pereira Maria A A, Fragoso Maria C B V, Hoff Ana O, Almeida Madson Q, Violante Alice H D, Quidute Ana R P, Zhang Zhewei, Recasens Mònica, Díaz Luis Robles, Kunavisarut Tada, Wannachalee Taweesak, Sirinvaravong Sirinart, Jonasch Eric, Grozinsky-Glasberg Simona, Fraenkel Merav, Beltsevich Dmitry, Egorov Viacheslav I, Bausch Dirk, Schott Matthias, Tiling Nikolaus, Pennelli Gianmaria, Zschiedrich Stefan, Därr Roland, Ruf Juri, Denecke Timm, Link Karl-Heinrich, Zovato Stefania, von Dobschuetz Ernst, Yaremchuk Svetlana, Amthauer Holger, Makay Özer, Patocs Attila, Walz Martin K, Huber Tobias B, Seufert Jochen, Hellman Per, Kim Raymond H, Kuchinskaya Ekaterina, Schiavi Francesca, Malinoc Angelica, Reisch Nicole, Jarzab Barbara, Barontini Marta, Januszewicz Andrzej, Shah Nalini, Young William F, Opocher Giuseppe, Eng Charis, Neumann Hartmut P H, Bausch Birke
Abstract excerpt
Pancreatic neuroendocrine tumors (PanNETs) are rare in von Hippel-Lindau disease (VHL) but cause serious morbidity and mortality. Management guidelines for VHL-PanNETs continue to be based on limited evidence, and survival data to guide surgical management are lacking. We established the European-American-Asian-VHL-PanNET-Registry to assess data for risks for metastases, survival and long-term outcomes to provide...
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