Article
Extensive pulmonary sarcoid reaction in a patient with BMPR-2 associated idiopathic pulmonary arterial hypertension.
Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG - 1 Aug 2016
Braam Evelien A J E, Quanjel Marian J R, Van Haren-Willems Jolanda H G M, Van Oosterhout Matthijs F M, Vink Aryan, Heijdra Yvonne F, Kwakkel-van Erp Johanna M
Abstract excerpt
Pulmonary arterial hypertension is a progressive life-threatening disease characterized by vascular remodeling. There is evidence that varied immune mechanism play an important role in progression of pulmonary hypertension. We describe a case of a 35-year-old woman with idiopathic pulmonary arterial hypertension (IPAH) and a novel BMPR2 mutation, who underwent a successful lung transplantation. Extensive...
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