Article
Atypical fibroxanthoma arising in a young patient with Li-Fraumeni syndrome.
Journal of cutaneous pathology - 1 Mar 2014
Lee Sun Mi, Zhang Wei, Fernandez Martin P
Abstract excerpt
Patients with Li-Fraumeni syndrome (LFS) have a germ-line mutation of p53 (TP53) and are predisposed to develop a variety of malignancies at an early age. In this report, we describe an 18-year-old woman with LFS who developed an atypical fibroxanthoma (AFX) on her left arm. This tumor was based in the dermis, sparsely cellular and had ill-defined borders. It was composed predominantly of medium-sized...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.
