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Article

ACAD9, a complex I assembly factor with a moonlighting function in fatty acid oxidation deficiencies.

Human molecular genetics - 1 Mar 2014

Nouws Jessica, Te Brinke Heleen, Nijtmans Leo G, Houten Sander M

Abstract excerpt

Oxidative phosphorylation and fatty acid oxidation are two major metabolic pathways in mitochondria. Acyl-CoA dehydrogenase 9 (ACAD9), an enzyme assumed to play a role in fatty acid oxidation, was recently identified as a factor involved in complex I biogenesis. Here we further investigated the role of ACAD9's enzymatic activity in fatty acid oxidation and complex I biogenesis. We provide evidence indicating that...

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Source

Identifiers

PMID: 24158852
DOI: 10.1093/hmg/ddt521

Genes

ACAD9

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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ACAD9, a complex I assembly factor with a moonlighting function in fatty acid oxidation deficiencies.PMID 24158852Read ↗

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