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Article

Neurobehavioral features and natural history of juvenile neuronal ceroid lipofuscinosis (Batten disease).

Journal of child neurology - 1 Sept 2013

Adams Heather R, Mink Jonathan W

Abstract excerpt

Juvenile neuronal ceroid lipofuscinosis is a childhood-onset neurodegenerative disease with prominent symptoms comprising a pediatric dementia syndrome: intellectual decline, mood and behavioral impairments, and loss of adaptive skills. We review the history of neurobehavioral features in juvenile neuronal ceroid lipofuscinosis and the work of the University of Rochester Batten Center to characterize the extent...

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Identifiers

PMID: 24014508
DOI: 10.1177/0883073813494813
PMCID: PMC3976549

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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