Article
[Liver diseases in alpha 1 antitrypsin deficiency syndrome in children].
Gastroenterologisches Journal : Organ der Gesellschaft fur Gastroenterologie der DDR - 1 Jan 1990
Cario W R
Abstract excerpt
About 15% of children with alpha-1-antitrypsin-deficiency with proteinase inhibitor type ZZ develop hepatopathy, uninfluenceable in its course. These children already show symptoms of severe cholestatic hepatitis in early infancy as became obvious from data of 13 children being patients in the au...
Topics
- Adolescent
- Biopsy
- Child
- Child, Preschool
- Combined Modality Therapy
- Female
- Follow-Up Studies
- Humans
- Infant
- Infant, Newborn
- Jaundice, Neonatal
- Liver
- Liver Cirrhosis, Biliary
- Liver Function Tests
- Male
- Phenotype
- alpha 1-Antitrypsin Deficiency