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Article

Lipid metabolism in cystic fibrosis

7 Feb 2009

Abstract excerpt

PURPOSE OF REVIEW: Expression of defective cystic fibrosis transmembrane conductance regulator (CFTR), the cause for cystic fibrosis, affects fatty acid, cholesterol and sphingolipid metabolism. This review summarizes recent observations and evaluates current understanding of mechanisms. RECENT FINDINGS: Recent observations implicate CFTR, in addition to known effects on fatty acid and cholesterol metabolism, in...

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Share to Cystic Fibrosis Research Advances
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PMID: 19209467
DOI: 10.1097/mco.0b013e32832595b7

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