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Article

Phenotypic behavior of C2C12 myoblasts upon expression of the dystrophy-related caveolin-3 P104L and TFT mutants.

FEBS letters - 30 Oct 2007

Fanzani Alessandro, Stoppani Elena, Gualandi Laura, Giuliani Roberta, Galbiati Ferruccio, Rossi Stefania, Fra Anna, Preti Augusto, Marchesini Sergio

Abstract excerpt

Caveolin-3 (Cav-3) is the main scaffolding protein present in myofiber caveolae. We transfected C2C12 myoblasts with dominant negative forms of Cav-3, P104L or DeltaTFT, respectively, which cause the limb-girdle muscular dystrophy 1-C. Both these forms triggered Cav-3 loss during C2C12 cell diffe...

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Identifiers

PMID: 17935719
DOI: 10.1016/j.febslet.2007.09.055

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 2 Sept 2026. Prepared record publication-17935719-2026-09-02.2. Manifest publication-graph-cohort-2026-09-02.2.

Source receipt: PubMed via Helena Literature Corpus, retrieved 2 Sept 2026.

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