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Article

Severe congenital neutropenia.

Seminars in hematology - 1 Jul 2006

Welte Karl, Zeidler Cornelia, Dale David C

Abstract excerpt

Severe congenital neutropenia (CN) includes a variety of hematologic disorders characterized by severe neutropenia, with absolute neutrophil counts (ANC) below 0.5 x 10(9)/L, and associated with severe systemic bacterial infections from early infancy. One subtype of CN, Kostmann syndrome, is an autosomal recessive disorder, characterized histopathologically by early-stage maturation arrest of myeloid...

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Identifiers

PMID: 16822461
DOI: 10.1053/j.seminhematol.2006.04.004

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