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Article

Molecular characterization of the genetic lesion in Dystonia musculorum (dt-Alb) mice.

Brain research - 6 Apr 2007

Goryunov Dmitry, Adebola Adijat, Jefferson Julius J, Leung Conrad L, Messer Anne, Liem Ronald K H

Abstract excerpt

Dystonia musculorum (dt) is an inherited autosomal recessive neuropathy in mice. Homozygous animals display primarily sensory neurodegeneration resulting in a severe loss of coordination. Several dt strains exist, including spontaneous mutants dt-Alb (Albany), dt-J (Jackson Labs), and dt-Frk (Frankel), and a transgene insertion mutant, Tg4. They contain mutations in the gene encoding Bullous Pemphigoid Antigen 1...

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Identifiers

PMID: 16725123
DOI: 10.1016/j.brainres.2006.04.068

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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