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Article

A case of Papillon-Lefevre syndrome associated with xanthogranulomatous pyelonephritis and hepatitis.

The Journal of dermatology - 1 Jan 2006

Mansur A Tülin, Göktay Fatih, Demirok Nüket

Abstract excerpt

Papillon-Lefevre syndrome (PLS) is an autosomally recessive palmoplantar keratoderma accompanied by psoriasiform plaques on the extensor surfaces of extremities and leading to premature loss of deciduous and permanent teeth by progressive periodontitis. Patients with PLS may exhibit mental retardation, intracranial ectopic calcifications, nail dystrophies and a tendency to various infectious disorders, in...

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Identifiers

PMID: 16469088
DOI: 10.1111/j.1346-8138.2006.00012.x

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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