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Article

Alpha-dystroglycan, the usual suspect?

Neuromuscular disorders : NMD - 1 Dec 2005

Brancaccio Andrea

Abstract excerpt

An increasing number of congenital muscular dystrophies might originate from genetic abnormalities of glycosyltransferases genes which are believed to target the alpha subunit of the dystroglycan (DG) adhesion complex as their major enzymatic substrate. alpha-DG is highly glycosylated and peripherally associated with the sarcolemma of skeletal muscle and the plasma membrane in a wide variety of cells. Several...

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PMID: 16289897
DOI: 10.1016/j.nmd.2005.08.003

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 6 Sept 2026. Manifest publication-graph-cohort-2026-09-06.1.

Source receipt: pubmed, retrieved 6 Sept 2026.

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