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Article

Long-term prognosis and causes of death in CADASIL: a retrospective study in 411 patients.

Brain : a journal of neurology - 1 Nov 2004

Opherk Christian, Peters Nils, Herzog Jürgen, Luedtke Rainer, Dichgans Martin

Abstract excerpt

Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL) is a hereditary angiopathy caused by mutations in the NOTCH3 gene. The clinical course is highly variable. Little is known about the long-term prognosis and the causes of death in CADASIL patients...

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Source

Identifiers

PMID: 15364702
DOI: 10.1093/brain/awh282

Genes

NOTCH3

Provenance

PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 1 Sept 2026. Prepared record publication-15364702-2026-09-01.1. Manifest publication-graph-cohort-2026-09-01.1.

Source receipt: PubMed via Helena Literature Corpus, retrieved 1 Sept 2026.

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Long-term prognosis and causes of death in CADASIL: a retrospective study in 411 patients.PMID 15364702Read ↗

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