Article
Adult-onset familial pulmonary fibrosis in Japanese brothers.
Pathology international - 1 Jan 2004
Yoshioka Yasuko, Saiki Shigeki, Tsutsumi-Ishii Yuko, Koyama Ryo, Hirashima Naoko, Harada Norihiro, Yamasaki Shigetaka, Suda Koichi, Fukuchi Yoshinosuke
Abstract excerpt
Two Japanese brothers were diagnosed in their 20s with familial pulmonary fibrosis, the pathological findings of which were consistent with usual interstitial pneumonia (UIP). However, an atypical characteristic was observed in the lungs of these brothers; 2-mm areas of 'honeycomb' were identified throughout the lungs, which is smaller than the generally observed 5-10 mm honeycombing seen in UIP. Fibroblastic...
Read the complete abstract on PubMedTopics
Share this publication in a Topic to start or enrich a Post.