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Article

Clinical features and genetic analysis of surfactant protein C in adult-onset familial interstitial pneumonia.

Respirology (Carlton, Vic.) - 1 Jan 2006

Setoguchi Yasuhiro, Ikeda Tomomi, Fukuchi Yoshinosuke

Abstract excerpt

Familial cases of interstitial pneumonia (FIP) have been reported to be linked to mutations of the surfactant protein C (SP-C) gene. Based on this knowledge, we evaluated the characteristics of patients with adult-onset FIP in the Tokyo area using clinical and radiopathological findings, and further evaluated the genetic background of patients with FIP compared with sporadic IP patients using genetic sequencing...

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Identifiers

PMID: 16423270
DOI: 10.1111/j.1440-1843.2006.00807.x

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

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