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Article

Dysferlin expression after normal myoblast transplantation in SCID and in SJL mice.

Neuromuscular disorders : NMD - 1 Feb 2002

Leriche-Guérin K, Anderson L V B, Wrogemann K, Roy B, Goulet M, Tremblay J P

Abstract excerpt

Limb girdle muscular dystrophy type 2B form and Miyoshi myopathy are both caused by mutations in the recently cloned gene dysferlin. In the present study, we have investigated whether cell transplantation could permit dysferlin expression in vivo. Two transplantation models were used: SCID mice transplanted with normal human myoblasts, and SJL mice, the mouse model for limb girdle muscular dystrophy type 2B and...

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Source

Identifiers

PMID: 11738359
DOI: 10.1016/s0960-8966(01)00254-1

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-07.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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