Article

Anaesthetic management in Pelizaeus-Merzbacher disease -- a case report.

2022-03-31

Abstract excerpt

Pelizaeus-Merzbacher Disease (PMD) is a rare genetic disorder affecting brain and spinal cord. We report a 11-year-old child with PMD with multiple caries for teeth extraction under general anaesthesia. Prolonged neuromuscular blockade is of major concern in these patients and hence the importance of appropriate neuromuscular blockade management during procedure.

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Literature Corpus work: e24b7e66-bf2b-5074-88e9-20da095d7b64
DOI: 10.22541/au.164873484.47131939/v1

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