Article
Prospective Cardiovascular Magnetic Resonance Imaging in Adults with Alström Syndrome: Silent Progression of Diffuse Interstitial Fibrosis.
2020-06-29
Abstract excerpt
<title>Abstract</title> <p><bold>Background </bold>Alström syndrome (ALMS) is a rare ciliopathy characterised by early onset insulin resistance, obesity, and dyslipidaemia and is a model for diseases that have huge social, health and economic impact. Cardiomyopathy develops in the majority, with high rates of morbidity and mortality, the definitive features of which are coarse replacement fibrosis and diffuse myo...
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Identifiers and source
- Literature Corpus work
- d3ac8411-cc77-570b-88db-e184b4aea245
- DOI
- 10.21203/rs.3.rs-21122/v3