Article

An extra-glossal ectomesenchymal chondromyxoid tumor with RREB1::MRTFB fusion-positive: A case report of a rare tumor at a rare site

2024-11-01

Abstract excerpt

<title>Abstract</title> Background: Ectomesenchymal chondromyxoid tumor (ECT) is a rare benign intraoral tumor which almost exclusively presents as a small mass of the anterior dorsal tongue. Recently, the RREB1–MRTFB (previously known as MKL2) fusion gene has been identified in 90% of ECTs, all located in the tongue, emphasizing its genetic distinctiveness. Herein we report one mesenchymal tumor involving the...

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Literature Corpus work: 989aafa8-a9ce-5ce1-b9ba-bf0c353b5866
DOI: 10.21203/rs.3.rs-5283364/v1

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