Article

Multisystem Caliber-Persistent Arteriopathy Syndrome: A Novel Congenital Vasculopathy Associated with a Risk of Multiorgan Hemorrhage

2025-12-10

Abstract excerpt

<title>Abstract</title> <p> This study delineates a novel multisystem caliber-persistent arteriopathy syndrome, fundamentally redefining the classical Dieulafoy's lesion from a localized gastrointestinal anomaly to a systemic congenital vasculopathy. Through integrated histopathological and genomic analysis of a forensic autopsy case, we identified pervasive arterial remodeling across seven organ systems— charac...

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Literature Corpus work: 8bd567ed-0640-5412-9054-318e8861adf0
DOI: 10.21203/rs.3.rs-8074903/v1

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