Article

Long-Term Kidney Function Stabilization with Fludrocortisone in Autosomal Recessive Tubular Dysgenesis: A Case Report

2025-05-09

Abstract excerpt

<title>Abstract</title> <p>Renal tubular dysgenesis (RTD) is a rare disorder characterized by impaired development of the proximal tubules and renal dysfunction due to decreased fetal renal plasma flow and renin-angiotensin system (RAS) inhibition. Fetal anuria causes severe oligohydramnios and Potter sequence, and most patients die within days after birth due to refractory hypotension, anuria, and respiratory di...

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Literature Corpus work: 5b9337f6-7c3c-5521-9ba8-fd3796bff569
DOI: 10.21203/rs.3.rs-6586160/v1

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