Article

Pulmonary exacerbations in patients with genetically confirmed PCD: A prospective observational multicentre study

2025-11-19

Abstract excerpt

<h4>ABSTRACT</h4> <h4>Background</h4> Primary ciliary dyskinesia (PCD) is a rare genetic disorder characterized by deficient mucociliary clearance and development of chronic lung disease. Pulmonary exacerbations (PEx) in chronic lung diseases increase morbidity and lung function decline, but their frequency in PCD has been understudied. We aimed to prospectively determine the annual frequency of PEx in PCD and i...

Topics

Open a Topic to create a Post that cites this publication.

Identifiers and source

Literature Corpus work: 53e6fc0c-bc26-5ea7-8c5f-114dbc3559d3
DOI: 10.1101/2025.11.18.25340347

Open publication

Related research

Semantic proximity does not establish scientific evidence.

Click a neighbor to travelStep 1 · 12 closest

Pulmonary exacerbations in patients with genetically confirmed PCD: A prospective observational multicentre studyDOI 10.1101/2025.11.18.25340347Read

Primary Ciliary Dyskinesia: An Update on Clinical Aspects, Genetics, Diagnosis, and Future Treatment StrategiesSemantic proximity Read

Primary Ciliary Dyskinesia in Adult Bronchiectasis: Data from the German Bronchiectasis Registry PROGNOSIS.Semantic proximity Read

The international primary ciliary dyskinesia cohort (iPCD Cohort): methods and first results.Semantic proximity Read

Chronic airway disease in primary ciliary dyskinesia-spiced with geno-phenotype associations.Semantic proximity Read

Diagnosis and management of primary ciliary dyskinesiaSemantic proximity Read

Clinical characteristics, functional respiratory decline and follow-up in adult patients with primary ciliary dyskinesia.Semantic proximity Read

Clinical manifestations and genotype of primary ciliary dyskinesia diagnosed in Korea: a nationwide, multicenter, retrospective studySemantic proximity Read

Clinical and genetic spectrum of primary ciliary dyskinesia in Chinese patients: a systematic review.Semantic proximity Read

Clinical phenotypes of primary ciliary dyskinesia.Semantic proximity Read

Long-term Azithromycin Treatment in Pediatric Primary Ciliary Dyskinesia: A Retrospective StudySemantic proximity Read

Clinical and Genetic Spectrum of Children With Primary Ciliary Dyskinesia in China.Semantic proximity Read

Clinical Manifestations and Genotype of Primary Ciliary Dyskinesia Diagnosed in Korea: Multicenter StudySemantic proximity Read