Article

A Multicenter Study On Quality Of Life of The “Greater Patient” In Congenital Ichthyoses

2021-05-11

Abstract excerpt

<title>Abstract</title> <p><bold>Background</bold>: Autosomal recessive congenital ichthyoses (ARCI) are a genetically heterogeneous group of rare and chronic disorders characterized by generalized skin scaling and hyperkeratosis, erythroderma, and palmoplantar keratoderma. Additional features include ectropion, eclabium, ear deformities, foul-smell, joints contractures and walking problems, recurrent infections,...

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Literature Corpus work: 026d8e29-4ab7-5408-814d-175f2267d3af
DOI: 10.21203/rs.3.rs-489315/v1

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