Article
Antineutrophil cytoplasmic autoantibodies (ANCA) in children with cystic fibrosis.
Journal of autoimmunity - 1 Apr 1998
Sedivá A, Bartůnková J, Kolárová I, Hrusák O, Vávrová V, Macek M, Lockwood C M, Dunn A C
Abstract excerpt
Anti-neutrophil cytoplasmic antibodies (ANCA) represent a useful diagnostic tool in patients with small vessel vasculitis. Circulating ANCA specific for bactericidal/permeability increasing protein (BPI) have been recently reported in adult patients with cystic fibrosis (CF), an autosomal recessi...
Topics
- Adolescent
- Age Factors
- Antibodies, Antineutrophil Cytoplasmic
- Antibody Specificity
- Antimicrobial Cationic Peptides
- Autoantigens
- Autoimmune Diseases
- Blood Proteins
- Child
- Child, Preschool
- Cystic Fibrosis
- Cystic Fibrosis Transmembrane Conductance Regulator
- Disease Progression
- Enzyme-Linked Immunosorbent Assay
- Female
- Fluorescent Antibody Technique, Indirect
- Genotype
- Humans
