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Article

Mouse models of human lysosomal diseases.

Brain pathology (Zurich, Switzerland) - 1 Jan 1998

Suzuki K, Proia R L, Suzuki K

Abstract excerpt

Genetically authentic animal models of human lysosomal diseases occur spontaneously in many mammalian species. However, most are among larger domestic or farm animals with only two well-defined genetic lysosomal diseases known among rodents. This status changed dramatically in recent years with the advent of the combined homologous recombination and embryonic stem cell technology, which allows directed generation...

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Identifiers

PMID: 9458176
DOI: 10.1111/j.1750-3639.1998.tb00145.x
PMCID: PMC8098314

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

Source receipt: pubmed, retrieved 7 Sept 2026.

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