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Article

Systemic necrotizing vasculitides in severe alpha1-antitrypsin deficiency.

QJM : monthly journal of the Association of Physicians - 1 Aug 1996

Mazodier P, Elzouki A N, Segelmark M, Eriksson S

Abstract excerpt

We describe the clinical presentation and outcome in a series of eight patients with systemic necrotizing vasculitis and severe alpha1-antitrypsin (AAT) deficiency followed up at three Swedish hospitals during 1968-92. We also review six other cases reported in the literature during the same period. Diagnosis of severe AAT deficiency was based on the presence of the PiZZ phenotype, or low plasma total trypsin...

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PMID: 8935481
DOI: 10.1093/qjmed/89.8.599

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PubMed metadata and Literature Corpus relationships. Corpus snapshot updated 7 Sept 2026. Manifest publication-graph-cohort-2026-09-08.1.

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